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Diseases » Caroli Disease » Summary

What is Caroli Disease?

Contents

Caroli Disease: Introduction
Prognosis
Other names for Caroli Disease
What are the symptoms of Caroli Disease?
How is it treated?
Caroli Disease: Introduction

What is Caroli Disease?

Caroli Disease: A rare disorder where the bile ducts inside the liver become enlarged resulting in infection, irritation and gallstone formation.
Caroli Disease: Congenital cystic dilatation of the intrahepatic bile ducts (BILE DUCTS, INTRAHEPATIC). It consists of 2 types: simple Caroli disease is characterized by bile duct dilatation (ectasia) alone; and complex Caroli disease is characterized by bile duct dilatation with extensive hepatic fibrosis and portal hypertension (HYPERTENSION, PORTAL). Benign renal tubular ectasia is associated with both types of Caroli disease.
Source - Diseases Database

Caroli Disease is listed as a "rare disease" by the Office of Rare Diseases (ORD) of the National Institutes of Health (NIH). This means that Caroli Disease, or a subtype of Caroli Disease, affects less than 200,000 people in the US population.
Source - National Institutes of Health (NIH)

Ophanet, a consortium of European partners, currently defines a condition rare when it affects 1 person per 2,000. They list Caroli Disease as a "rare disease".
Source - Orphanet

Caroli Disease: Introduction

How serious is Caroli Disease?

Complications of Caroli Disease: see complications of Caroli Disease

What are the symptoms of Caroli Disease?

Symptoms of Caroli Disease: see symptoms of Caroli Disease

Complications of Caroli Disease: see complications of Caroli Disease

How is it treated?

Treatments for Caroli Disease: see treatments for Caroli Disease
Research for Caroli Disease: see research for Caroli Disease

Name and Aliases of Caroli Disease

Main name of condition: Caroli Disease

Other names or spellings for Caroli Disease:

congenital biliary ectasias, acute cholangitis, congenital dilatation of intrahepatic bile ducts, Congenital polycystic dilatation of intrahepatic bile ducts, Caroli disease isolated, Cystic dilatation of the intrahepatic biliary tree

Congenital dilatation of lobar intrahepatic bile duct Source - Diseases Database

Caroli disease isolated, Congenital polycystic dilatation of intrahepatic bile ducts, Cystic dilatation of the intrahepatic biliary tree
Source - Office of Rare Diseases (ORD) of the National Institutes of Health (NIH)

Research the causes of these diseases that are similar to, or related to, Caroli Disease: