Prevalence and Incidence of Empty Sella Syndrome

Prevalance of Empty Sella Syndrome:

rare ... see also overview of Empty Sella Syndrome.

Empty Sella Syndrome: Rare Disease

Empty Sella Syndrome is listed as a "rare disease" by the Office of Rare Diseases (ORD) of the National Institutes of Health (NIH). This means that Empty Sella Syndrome, or a subtype of Empty Sella Syndrome, affects less than 200,000 people in the US population.

Prevalence/Incidence of Empty Sella Syndrome: Online Medical Books

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Secondary polycythemia: Causes and incidence
(Professional Guide to Diseases (Eighth Edition))

Secondary polycythemia may result from increased production of erythropoietin. This hormone, which is possibly produced and secreted in the kidneys, stimulates bone marrow production of RBCs. Increased production may be a compensatory physiologic response to hypoxemia, which may result from:

❑ chronic obstructive pulmonary disease

❑ hemoglobin (Hb) abnormalities (such as carboxyhemoglobinemia, which is seen in heavy smokers)

❑ heart failure (causing a decreased ventilation-perfusion ratio)

❑ right-to-left shunting of blood in the heart (as in transposition of the great vessels)

❑ central or peripheral alveolar hypoventilation (as in barbiturate intoxication or pickwickian syndrome)

❑ low oxygen content at high altitudes.

Increased production of erythropoietin may also be an inappropriate (pathologic) response to renal disease (such as renal vascular impairment, renal cysts, or hydronephrosis), to central nervous system disease (such as encephalitis and parkinsonism), to neoplasms (such as renal tumors, uterine myomas, or cerebellar hemangiomas), or to endocrine disorders (such as Cushing’s syndrome, Bartter’s syndrome, or pheochromocytomas). Rarely, secondary polycythemia results from a recessive genetic trait.

Secondary polycythemia occurs in approximately 2 out of every 100,000 people living at or near sea level; incidence rises among those living at high altitudes.

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Source: Professional Guide to Diseases (Eighth Edition), 2005

About prevalence and incidence statistics:

The term 'prevalence' of Empty Sella Syndrome usually refers to the estimated population of people who are managing Empty Sella Syndrome at any given time. The term 'incidence' of Empty Sella Syndrome refers to the annual diagnosis rate, or the number of new cases of Empty Sella Syndrome diagnosed each year. Hence, these two statistics types can differ: a short-lived disease like flu can have high annual incidence but low prevalence, but a life-long disease like diabetes has a low annual incidence but high prevalence. For more information see about prevalence and incidence statistics.