What is Primary biliary cirrhosis?
What is Primary biliary cirrhosis?
- Primary biliary cirrhosis: Primary biliary cirrhosis is a chronic and progressive cholestatic disease of the liver.
- Primary biliary cirrhosis: a form of biliary cirrhosis in which small intrahepatic ducts are destroyed while the major intra and extra hepatic ducts remain patent; most patients are middle aged females and have circulating antimitochondrial antibodies.
Source - Diseases Database
Primary biliary cirrhosis is listed as a "rare disease" by the Office of
Rare Diseases (ORD) of the National Institutes of Health
(NIH). This means that Primary biliary cirrhosis, or a subtype of Primary biliary cirrhosis,
affects less than 200,000 people in the US population.
Source - National Institutes of Health (NIH)
Ophanet, a consortium of European partners,
currently defines a condition rare when it affects 1 person per 2,000.
They list Primary biliary cirrhosis as a "rare disease".
Source - Orphanet
Primary biliary cirrhosis: Introduction
Types of Primary biliary cirrhosis:
Broader types of Primary biliary cirrhosis:
How many people get Primary biliary cirrhosis?
Prevalance of Primary biliary cirrhosis: 9,232 people in the USA 1996 1
Prevalance Rate of Primary biliary cirrhosis: approx 1 in 29,462 or 0.00% or 9,231 people in USA [about data]
Who gets Primary biliary cirrhosis?
Patient Profile for Primary biliary cirrhosis: Typically age 30-60
Profile for Primary biliary cirrhosis:
The disease affects
women more often than men, and usually occurs between the ages of 30 and
60 years.
(Source: excerpt from Primary Biliary Cirrhosis: NIDDK)
Gender Profile for Primary biliary cirrhosis: Women 9:1 (NWHIC).
Gender Ratio for Primary biliary cirrhosis: female:male 10:1
How serious is Primary biliary cirrhosis?
Complications of Primary biliary cirrhosis:
see complications of Primary biliary cirrhosis
What causes Primary biliary cirrhosis?
Causes of Primary biliary cirrhosis: see causes of Primary biliary cirrhosis
Causes of Primary biliary cirrhosis:
The cause of primary biliary cirrhosis is unknown.
(Source: excerpt from Primary Biliary Cirrhosis: NIDDK)
Risk factors for Primary biliary cirrhosis:
see
risk factors for Primary biliary cirrhosis
What are the symptoms of Primary biliary cirrhosis?
Symptoms of Primary biliary cirrhosis:
see symptoms of Primary biliary cirrhosis
Complications of Primary biliary cirrhosis:
see complications of Primary biliary cirrhosis
Onset of Primary biliary cirrhosis: Primary biliary cirrhosis mostly affects middle-aged women, with a mean age of 39 years. Onset usually occurs in persons aged 30-65 years.
Can anyone else get Primary biliary cirrhosis?
Inheritance:
see inheritance of Primary biliary cirrhosis
Primary biliary cirrhosis: Testing
Diagnostic testing: see tests for Primary biliary cirrhosis.
Misdiagnosis: see misdiagnosis and Primary biliary cirrhosis.
How is it treated?
Treatments for Primary biliary cirrhosis:
see treatments for Primary biliary cirrhosis
Research for Primary biliary cirrhosis:
see research for Primary biliary cirrhosis
Organs Affected by Primary biliary cirrhosis:
Organs and body systems related to Primary biliary cirrhosis include:
Name and Aliases of Primary biliary cirrhosis
Main name of condition: Primary biliary cirrhosis
Class of Condition for Primary biliary cirrhosis: autoimmune possibly
Other names or spellings for Primary biliary cirrhosis:
PBC, Hanot syndrome, Hanot cirrhosis, Familial primary biliary cirrhosis
Chronic non-suppurative destructive cholangitis, PBC
Source - Diseases Database
Familial primary biliary cirrhosis, PBC, Familial primary biliary cirrhosis
Source - Office of Rare Diseases (ORD) of the National Institutes of Health (NIH)
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» Next page: Online Medical Textbooks for Primary biliary cirrhosis
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