Diseases » Primary pulmonary hypertension » Summary

What is Primary pulmonary hypertension?

Contents

Primary pulmonary hypertension: Introduction
Types of Primary pulmonary hypertension
Prognosis
Complications
Prevalence
Other names for Primary pulmonary hypertension
Who gets Primary pulmonary hypertension?
What causes Primary pulmonary hypertension?
What are the symptoms of Primary pulmonary hypertension?
Organs Affected by Primary pulmonary hypertension
Can anyone else get Primary pulmonary hypertension?
How is it treated?
Primary pulmonary hypertension: Introduction

What is Primary pulmonary hypertension?

Primary pulmonary hypertension: Primary pulmonary hypertension refers to high blood pressure in the arteries that carry blood to the lungs for no apparent reason. Blood pressure in other parts of the body is normal or sometimes even low.
Primary pulmonary hypertension: The presence of abnormal uterine bleeding immediately after LABOR, OBSTETRIC or childbirth.
Source - Diseases Database

Primary pulmonary hypertension is listed as a "rare disease" by the Office of Rare Diseases (ORD) of the National Institutes of Health (NIH). This means that Primary pulmonary hypertension, or a subtype of Primary pulmonary hypertension, affects less than 200,000 people in the US population.
Source - National Institutes of Health (NIH)

Primary pulmonary hypertension: Introduction

Types of Primary pulmonary hypertension:

Types of Primary pulmonary hypertension:

Familial PPH - inherited form; only about 6-10% of cases.
Sporadic PPH - non-inherited form.
more types...»

Broader types of Primary pulmonary hypertension:

How many people get Primary pulmonary hypertension?

Incidence (annual) of Primary pulmonary hypertension: 300 new cases annually (NHLBI)
Incidence Rate of Primary pulmonary hypertension: approx 1 in 906,666 or 0.00% or 300 people in USA [about data]
Incidence of Primary pulmonary hypertension: In the United States it has been estimated that 300 new cases of PPH are diagnosed each year; the greatest number are reported in women between the ages of 21 and 40. (Source: excerpt from NHLBI, Facts About Primary Pulmonary Hypertension: NHLBI)

Who gets Primary pulmonary hypertension?

Patient Profile for Primary pulmonary hypertension: Typically women 21-40 but any age possible.

Profile for Primary pulmonary hypertension: the greatest number are reported in women between the ages of 21 and 40. Indeed, at one time the disease was thought to occur among young women almost exclusively; we now know, however, that men and women in all age ranges, from very young children to elderly people, can develop PPH. Apparently it also affects people of all racial and ethnic origins equally. (Source: excerpt from NHLBI, Facts About Primary Pulmonary Hypertension: NHLBI)

Gender Profile for Primary pulmonary hypertension: Usually women but also occurs in men.

How serious is Primary pulmonary hypertension?

Prognosis of Primary pulmonary hypertension: Early detection and prompt treatment can significantly improve symptoms and long-term outcomes.
Complications of Primary pulmonary hypertension: see complications of Primary pulmonary hypertension

What causes Primary pulmonary hypertension?

Causes of Primary pulmonary hypertension: see causes of Primary pulmonary hypertension
Cause of Primary pulmonary hypertension: Unknown.
Risk factors for Primary pulmonary hypertension: see risk factors for Primary pulmonary hypertension