What is Schilder's Disease?
What is Schilder's Disease?
- Schilder's Disease: Rare nerve myelin condition.
- Schilder's Disease: A rare central nervous system demyelinating condition affecting children and young adults. Pathologic findings include a large, sharply defined, asymmetric focus of myelin destruction that may involve an entire lobe or cerebral hemisphere. The clinical course tends to be progressive and includes dementia, cortical blindness, cortical deafness, spastic hemiplegia, and pseudobulbar palsy. Concentric sclerosis of Balo is differentiated from diffuse cerebral sclerosis of Schilder by the pathologic finding of alternating bands of destruction and preservation of myelin in concentric rings. Alpers' Syndrome refers to a heterogeneous group of diseases that feature progressive cerebral deterioration and liver disease. (From Adams et al., Principles of Neurology, 6th ed, p914; Dev Neurosci 1991;13(4-5):267-73)
Source - Diseases Database
Schilder's Disease is listed as a "rare disease" by the Office of
Rare Diseases (ORD) of the National Institutes of Health
(NIH). This means that Schilder's Disease, or a subtype of Schilder's Disease,
affects less than 200,000 people in the US population.
Source - National Institutes of Health (NIH)
Ophanet, a consortium of European partners,
currently defines a condition rare when it affects 1 person per 2,000.
They list Schilder's Disease as a "rare disease".
Source - Orphanet
Schilder's Disease: Introduction
Types of Schilder's Disease:
Broader types of Schilder's Disease:
How many people get Schilder's Disease?
Prevalance of Schilder's Disease: rare
How serious is Schilder's Disease?
Prognosis of Schilder's Disease: Variable. Some people get remission, others get mild problems, others get severe, sometimes fatal.
Complications of Schilder's Disease:
see complications of Schilder's Disease
Prognosis of Schilder's Disease:
As
with multiple sclerosis, the course and prognosis of Schilder's disease
are unpredictable. For some individuals the disorder is progressive with a
steady, unremitting course. Others may experience significant improvement
and even remission. In some cases, Schilder's disease is fatal.
(Source: excerpt from NINDS Schilder's Disease Information Page: NINDS)
What causes Schilder's Disease?
Causes of Schilder's Disease: see causes of Schilder's Disease
Cause of Schilder's Disease: Loss or damage to myelin coating on nerves.
What are the symptoms of Schilder's Disease?
Symptoms of Schilder's Disease:
see symptoms of Schilder's Disease
Complications of Schilder's Disease:
see complications of Schilder's Disease
Schilder's Disease: Testing
Diagnostic testing: see tests for Schilder's Disease.
Misdiagnosis: see misdiagnosis and Schilder's Disease.
How is it treated?
Treatments for Schilder's Disease:
see treatments for Schilder's Disease
Prevention of Schilder's Disease:
see prevention of Schilder's Disease
Research for Schilder's Disease:
see research for Schilder's Disease
Organs Affected by Schilder's Disease:
Organs and body systems related to Schilder's Disease include:
Name and Aliases of Schilder's Disease
Main name of condition: Schilder's Disease
Other names or spellings for Schilder's Disease:
Myelinoclastic Diffuse Sclerosis, Diffuse Sclerosis
Diffuse sclerosis of Schilder, Balo's concentric sclerosis, Encephalitis periaxalis diffusa, Myelinoclastic diffuse sclerosis
Source - Diseases Database
Siemerling-Creutzfeldt disease, Adrenoleukodystrophy, AMN, Addison disease and cerebral sclerosis, Addison-Schilder syndrome, Adrenomyeloneuropathy, Bronze Schilder disease
Source - Office of Rare Diseases (ORD) of the National Institutes of Health (NIH)
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